Persistent Müllerian duct syndrome: A novel mutation in the Αnti-Müllerian Ηormone gene

Ayça Altincik, Fahri Karaca, Hüseyin Onay

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BACKGROUND AND OBJECTIVE: Persistent Müllerian duct syndrome (PMDS) is a relatively rare form of 46,XY disorder of sex development caused by the failure of formation, release or action of anti-Müllerian hormone (AMH) in intrauterine life. In this report we describe a case diagnosed with PMDS with a novel homozygous mutation in the AMH gene …